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Radiology · Neuroimaging: Chiari malformation
Sample itemA neonate with a lumbar myelomeningocele has MRI showing a small posterior fossa with cerebellar tonsils and vermis displaced through the foramen magnum and a beaked tectum. What is the diagnosis?
Original practice item, not a recalled exam question. Nothing here is recorded.
The answer and the reasoning
B. Chiari II malformation
Chiari II is nearly always associated with myelomeningocele and shows a small posterior fossa, caudal displacement of the vermis and medulla, beaked tectum and hydrocephalus. Chiari I has isolated tonsillar descent of more than 5 mm and presents in adults. Folic acid prevents neural tube defects.
Option by option
A. Arachnoid cyst
An arachnoid cyst is an extra-axial CSF collection.
B. Chiari II malformation (correct)
Correct. Myelomeningocele with tonsillar and vermian descent is Chiari II.
C. Chiari I malformation
Chiari I has only tonsillar descent without myelomeningocele.
D. Dandy-Walker malformation
Dandy-Walker has an enlarged posterior fossa with a cystic fourth ventricle.
Source note: Original NextPrep sample item — pending expert review. This item is original practice material awaiting independent expert review, so confirm important facts in a standard textbook.
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